CEREBELLAR HEMANGIOBLASTOMA IN A PATIENT WITH VON HIPPEL-LINDAU DISEASE : A CASE REPORT

Abstract

A 23 year-old Chinese woman presented with symptoms of increased intracranial pressure due to obstructive hydrocephalus as a sequel to a mass effect from cerebellar haemangioblastoma. She underwent removal of the right cerebellar haemangioblastoma and ventriculo-peritoneal shunting. She also had bilateral retinal haemangioblastoma, left renal carcinoma, renal and pancreatic cysts withoutphaeochromocytoma. A left partial nephrectomy was performed for renal cell carcinoma followed by radiotherapy. She survived the initial episode only to succumb to another cerebellar haemorrhage 18 months later.